Tetralogy of Fallot with Total Anomalous Pulmonary Venous Connection: A Rare Variant

Tetralogy of Fallot with total anomalous pulmonary venous connection is a rare entity. Due to disordered development of arterial and venous ends of the heart there is anomalous venous return coupled with outflow tract anomalies. Clinical manifestations are similar to classical Tetralogy of Fallot with masked findings of anomalous pulmonary venous return, thus posing challenge to clinicians. Preoperative diagnosis is mandatory as repair of both defects is required simultaneously.